Oral manifestations of Parry-Romberg syndrome

Authors

  • Irene Anto Sree Anjaneya Institute of Dental Sciences https://orcid.org/0000-0002-9935-7514
  • Joseph Johny Sree Anjaneya Institute of Dental Sciences
  • Neena Muneer Khan Sree Anjaneya Institute of Dental Sciences
  • Anjhana Narayanan Sree Anjaneya Institute of Dental Sciences

DOI:

https://doi.org/10.5935/2525-5711.20200003

Keywords:

Facial Hemiatrophy, Alopecia, Uveitis

Abstract

Introduction: Parry-Romberg syndrome (PRS) or Idiopathic hemifacial atrophy is a rare neurocutaneous syndrome, characterized by slowly progressive atrophy located on one side of the face, primarily involving the skin, fat and connective tissue and it becomes stable after certain time period. It exhibits many intraoral and extraoral features. The incidence and the causes of this changes remains unknown. Objective: We present this case report to improve the understanding of this rare condition. Case Report: We present a case of 33 year old male patient who reported to our department with progressive hemifacial atrophy on left side of the face, diagnosed as Parry-Romberg syndrome after clinical and radiographic examination. Conclusion: Parry-Romberg syndrome is a rare condition of progressive deformity of the face with various oral manifestations. It may also involve certain occular and neurological disturbances. The major treatment option is the esthetic management and other symptomatic treatments.

Author Biographies

Irene Anto, Sree Anjaneya Institute of Dental Sciences

Oral Medicine And Radiology, House Surgeon - Calicut - Kerala - Índia

Joseph Johny, Sree Anjaneya Institute of Dental Sciences

Oral Medicine And Radiology, Assistant Professor - Calicut - Kerala - Índia

Neena Muneer Khan, Sree Anjaneya Institute of Dental Sciences

Oral Medicine And Radiology, Assistant Professor - Calicut - Kerala - Índia

Anjhana Narayanan, Sree Anjaneya Institute of Dental Sciences

Periodontology, Assistant Professor - Calicut - Kerala - Índia

References

Parry-Romberg Syndrome.Available from:http://www.whonamedit.com/doctor.cfm [Last updated on 2009 Dec]

Miller MT, Sloane H, Goldberg MF, Grisolano J, Frenkel M, Mafee MF. Progressive hemifacial atrophy. J Pediatr Ophthamol Strabismus. 1987;24(1):27-36.

Whyman RA, Doyle TCA, Harding WJ, Ferguson MM. An unusual case of hemifacial atrophy. Oral Surg Oral Med Oral Pathol 1992;73:564-9.

Pinheiro TP, Silva CC, Silveira CS, Botelho PC, Pinheiro MG, PinheiroJde J. Progressive Hemifacial Atrophy--case report. Med Oral Patol Oral Cir Bucal. 2006 Mar 1; 11(2): E112-4. Review. [Medline: 16505785] [FREE Full Text]

Stone J. Parry-Romberg syndrome. Practical Neurology. 2006; 6: 185-188.

Tollefson MM, Witman PM. En coup de sabre morphea and Parry-Romberg syndrome: a retrospective review of 54 patients. J Am Acad Dermatol. 2007; 56 (2): 257-263.

Mazzeo N, Fisher JG, Mayer MH, Mathieu GP. Progressive hemifacial atrophy (Parry- Romberg Syndrome)- case report. Oral Surg Oral Med Oral Pathol Endod1995;79:30-5.

Pensler JM, Murphy GF, Mulliken JB. Clinical and ultrastructural studies of Romberg's hemifacial atrophy. Plast Reconstr Surg 1990;85:669-74.

Foster TD. The effects of hemifacial atrophy on dental growth. Br Dent J 1979;146:148-50

Glass D. Hemifacial atrophy. Br J Oral Surg 1964;1:194-9.

Roddi R, Riggio E, Gilbert PM, Hovius SE, Vaandrager JM, Van der Muelen JC.Clinical evaluation of techniques used in surgical treatment of Progressive hemifacial atrophy. J Craniomaxillofac Surg 1994;22:23-32.

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Published

2018-01-20

How to Cite

1.
Anto I, Johny J, Khan NM, Narayanan A. Oral manifestations of Parry-Romberg syndrome. J Oral Diagn [Internet]. 2018 Jan. 20 [cited 2024 Sep. 19];3:1-4. Available from: https://jordi.com.br/revista/article/view/170

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Section

Case Report