Christ-Siemens-Touraine Syndrome - A Case Report with Review of literature
DOI:
https://doi.org/10.5935/2525-5711.20200021Keywords:
Syndromic oligodontia, ectodermal dysplasia, hypohidrotic ectodermal dysplasiaAbstract
Ectodermal dysplasia (ED) is a hereditary disorder characterized by developmental defects of structures derived from the ectoderm. The most prevalent form of ED is hypohydrotic ectodermal dysplasia also known as Christ-Siemens-Touraine syndrome. This case report illustrates the manifestations and diagnosis of a twenty-two-year-old male patient with hypohydrotic ectodermal dysplasia with a brief review of literature.
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Copyright (c) 1969 Valen Dela D'souza, Prasanna Kumar Rao, Raghavendra Kini
This work is licensed under a Creative Commons Attribution 4.0 International License.
